Purpose:
To present a clinical series of pediatric patients with inflammatory myofibroblastic tumors (IMFTs) of bronchopulmonary origin, highlighting diagnostic and therapeutic strategies for achieving optimal outcomes.
Materials and Methods:
Between 2017 and [current year], eight patients (aged 8–17 years; male-to-female ratio 7:1) with histopathologically confirmed IMFT were treated at our institution. Preoperative biopsy confirmed the diagnosis in six cases. Tumor localization included the trachea (n=1), left main bronchus (n=1), and pulmonary parenchyma (n=6). Surgical interventions comprised:
Circular resection of the trachea/bronchi (n=2)
Thoracoscopic lobectomy (n=2)
Open thoracotomy lobectomy (n=1)
Thoracoscopic anatomical segmentectomy (n=2).
Three-dimensional modeling and augmented reality were utilized for preoperative planning and intraoperative navigation.
Results:
All procedures were completed without intraoperative complications (operative time: 80–190 minutes). R0 resection (margin-negative) was achieved in all cases, with no instances of residual disease. During follow-up (1–3 years), no recurrences were observed.
Conclusions:
IMFTs of the bronchopulmonary system are rare in pediatric populations. Radical surgical excision with clear margins remains the cornerstone of treatment, ensuring long-term remission and preventing recurrence. Minimally invasive techniques, supported by advanced imaging technologies, offer a safe and effective approach for resection.
Keywords: Inflammatory Myofibroblastic Tumors, thoracic surgery, Minimally invasive techniques, Three-dimensional modeling, augmented reality
Anahtar Kelimeler: