The physical features determining the sex of an individual are the karyotype, the internal and external sexual organs, the gonads and the secondary sexual characteristics which appear at puberty. Intersex conditions occur when there is a defect in the normal process of sexual maturation that results in abnormalities in any of these features. The management of these conditions is in the midst of great change. Every aspect is currently under review including diagnostic techniques, timing and nature of treatment including surgery, and information given to the patients. The true incidence of most of these conditions is unknown and great secrecy still surrounds them.
We present our experience in 45 cases after major surgical reconstruction for intersex anomalies. 30 patients assigned females, 18 are congenital adrenal hyperplasia patients (CAH), 15 patients assigned males, 16 patients waiting for major surgical reconstruction after completing all investigations, 5 patients assigned males and 11 patients assigned females.
We review the investigation protocol, surgical techniques, complications, outcome and patients and family satisfaction.
Keywords: Intersex, urogenital, reconstruction, children
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